Congenital vascular ring is a rare malformation of aortic arch anomalies. The embryonic development of vascular rings is complex with diverse forms. In addition, vascular rings may associate with chromosome abnormalities. It is challenging for obstetric sonographers to make a correct diagnosis. As commonly used in cardiac examination, fetal echocardiography plays a key role in the screening and diagnosis of congenital heart disease. In the current review, we summarized the prenatal diagnosis of vascular ring by two and three-dimensional echocardiography. The differential diagnosis and prognosis of this rare abnormality were also commented.