| 摘要: |
| 目的 分析儿童永存左上腔静脉合并先天性心脏病类型的分布特征及发生率。 方法 对2013年至2017年北京儿童医院1676例永存左上腔静脉患儿的超声心动图资料及临床资料进行回顾性分析。 结果 永存左上腔静脉的检出率约0.79%(1676/212309),其中Ⅰ型永存左上腔静脉最常见约占99.7%(1671/1676)。永存左上腔静脉在先天性心脏病儿童中的检出率约3.0%(866/28403)。1676例永存左上腔静脉的患儿中,合并先天性心脏心脏病的患儿866例(51.7%),常见合并的先天性心脏病依次是室间隔缺损202例(23.3%)、房间隔缺损149例(17.2%)、法洛四联症73例(8.4%)、动脉导管未闭58例(6.7%)、主动脉该缩窄及主动脉缩窄复合畸形52例(6.0%)、心内膜垫缺损34例(4.0%)、右室双出口29例(3.3%)。 结论 永存左上腔静脉常合并先天性心脏大血管畸形,应提高对永存左上腔静脉合并先天性心脏病类型分布特征的认识,行超声心动图检查时正确诊断永存左上腔静脉及其合并畸形能够为临床制定患儿治疗方案提供可靠依据。 |
| 关键词: 永存左上腔静脉 先天性心脏病 超声心动图描记术 |
| DOI： |
| 投稿时间：2018-12-31修订日期：2019-01-22 |
| 基金项目: |
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| Persistent left superior vena cava accompanying congenital heart disease detected using echocardiography in children: Experience of a single center |
| YANG Jiao,MA Ning |
| (Department of Echocardiography,Beijing Children’s Hospital,Capital Medical University,National Center for Children’s Health) |
| Abstract: |
| Objective This study focuses on determining concomitant congenital heart disease in patents with persistent left superior vena cava. Methods The data of ulrasonic diagnosis and clinical date of 1676 children with persistent left superior vena cava were analyzed between 2013 and 2017. Result The incidence of persistent left superior vena cava was 0.79% (1676/212309) in all patients, and type I permanent left superior vena cava is the most common accounting for 9.7% (1671/1676). The incidence of persistent left superior vena cava was 3.0% (866/28403) in children with congenital heart disease. A total of 1676 patents with persistent left superior vena cava, 866 (51.7%) of whom were diagnosed with congenital heart disease. Of all the 1676 cases, the common concomitant congenital heart disease were ventricular septal defect (202, 23.3%), atrial septal defect (149, 17.2%), tetralogy of Fallot (73, 8.4%), patent ductus arteriosus (58,6.7%), isolated aortic coarctation and the aortic coarctation complex (52, 6.0%), endocardial pad defect (34,4.0%), double outlet right ventricle (29, 3.3%). Conclusion Increased awareness about the associaton of certain congenital heart disease with persistent left superior vena cava and a careful echocardiographic examinaton can facilitate the diagnosis of left superior vena cava. In additon, precise prior diagnosis of persistent left superior vena cava and its associated deformities can provide a reliable basis of the treatment. |
| Key words: Persistent left superior vena cava Congenital heart disease Echocardiography |
