| 摘要: |
| 肺动脉吊带(Pulmonary Artery Sling,PAS)是一种罕见的先天性血管畸形,又名迷走左肺动脉,常合并有包括气道狭窄、支气管桥、气管性支气管、先天性心脏病、先天性肛门闭锁、基因染色体病等多种单系统或多系统并发症。本文就肺动脉吊带的病因、病理机制、分型、临床表现及诊治方法做一简要综述。 |
| 关键词: 肺动脉吊带 胚胎发育 血管环 气管发育畸形 诊治 |
| DOI： |
| 投稿时间：2018-11-17修订日期：2019-05-27 |
| 基金项目:重庆市科学技术委员会社会事业与民生保障科技创新专项（cstc2016shmszx130009） |
|
| Advances in diagnosis and therapy of pulmonary artery sling |
| Hejie,Jixiaojuan |
| (Children''s Hospital of Chongqing Medical University) |
| Abstract: |
| Pulmonary Artery Sling(PAS) is a rare congenital vascular disease, which complied with airway stenosis, bridging bronchus, congenital heart disease and congenital anal atresia. As we known, it sometimes combined with several complex malformations. Children with PAS, especially with special facial features and other system malformation, should be alerted that the genes-chromosome lesions happened. We reviewed PAS for the definition, pathological mechanism, diagnosis and therapy in this article. |
| Key words: Pulmonary artery sling Embryonic development Vascular ring Tracheal malformation Diagnosis and treatment |
